Visual Field Defect of Patients with Retinitis Pigmentosa in Koreans

Hwang, Joon Seo; Yu, Hyeong Gon

Original Article

Korean Journal of Optometry and Vision Science 2012;11(1):42-47.
Published online June 20, 2012.

한국인 망막색소변성 환자의 시야장애의 평가

황준서, 유형곤

Department of Ophthalmology, Seoul National University College of Medicine, Seoul, Korea

Visual Field Defect of Patients with Retinitis Pigmentosa in Koreans

Joon Seo Hwang, Hyeong Gon Yu

Abstract

Purpose
To evaluate visual field defect of Korean patients with retinitis pigmentosa (RP). Methods: A total of 400 patients with RP who were diagnosed within 3 years, 231 males and 169 females were included in this study. Data were collected including age, symptomatic disease duration, family history, visual acuity (VA), Goldmann visual field (VF) at the initial visit. Results: Determination of inheritance pattern revealed 17.0% autosomal dominant RP cases, 11.5% autosomal recessive (AR) RP, 3.5% X-linked recessive (XL) RP, and 68.0% simplex RP, indicating a relative small proportion of AR RP cases. The remaining visual filed was ≥50^o (radius) in 7.3%, 25∼50^o in 10.8%, 10∼25^o in 29.3% and ≤10^o in 52.8%. Visual acuity was ≥20/30 in 43.8%, 20/100∼20/30 in 44.5%, 20/200∼20/100 in 5.5% and ≤20/200 in 6.3%. The functional acuity score of 83.3±17.2 was higher than the functional field score of 49.9±20.5. VA and VF defects were greater in AR RP and XL RP than in other types, the proportion of ≥20/30 VA was smaller and there was no patient who had VF greater than 25^o. Conclusions: Korean RP patients had advanced visual field defect at the initial visit. VF defect was greater than VA loss and more severe in the patient with AR RP and XL RP. (Korean J Optom Vis Sci 2012; 11(1):42-47)

Key Words: Retinal degeneration, Retinitis pigmentosa, Visual field, Koreans